The device itself looks really sexy, no doubt about that.
Looking more at the specs though it really seems more like a mobile device with a giant screen bolted on. It has as mentioned a 2TB laptop drive (probably) but even worse to me, the GTX 980M instead of the GTX 1080... if I'm going to go with a desktop over a laptop I really could use that extra boost (nearly twice as much processing power).
Yes the 1080 card is damn large but so fast they should have built the base around it, the base could easily be a bit larger without compromising the design.
I was pricing building out a desktop for VR work and as cool as this looks, it's not compelling as a replacement to the system I was thinking of building.
I'm also not 100% sure that an on-screen dial is superior to a dial accessory that sits of the desk (there are a number of USB dials I believe, I have one). It seems like it would take up a lot of screen real-estate and mandate the screen be tilted with you standing over it, not how most people work. Not to mention if you didn't have long arms, could you even reach across it easily? Even in the demo video some of the people seem to be stretching a lot.
I don't mean to throw so much shade onto a very cool device, I just wonder how it will be to use in practice when the novelty wears off. I'm sure some artists will really, really love this though.